DES (Desmin ) monoclonal Antibody | MB63007

DES (Desmin ) monoclonal Antibody | MB63007 | Gentaur UK, US & Europe Distribution

Host: Mouse

Reactivity: Human, Mouse, Rat

Application: FC, IHC, WB

Application Range: WB 1:200~500, IHC 1:150, FLOW 1:100

Background: This gene encodes a muscle-specific class III intermediate filament. Homopolymers of this protein form a stable intracytoplasmic filamentous network connecting myofibrils to each other and to the plasma membrane. Mutations in this gene are associated with desmin-related myopathy, a familial cardiac and skeletal myopathy (CSM), and with distal myopathies. [provided by RefSeq, Jul 2008]

Storage & Stability: PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Specificity: desmin

Molecular Weight: 53.4 kDa (Predicted)

Note: For research use only, not for use in diagnostic procedure.

Alternative Names: CSM1; CSM2; LGMD2R

Immunogen: Human fragment corresponding to amino acids 104-391 of human DES (NP_001918) produced in E.coli.

Conjugate: Unconjugated

Modification: Unmodification

Purification & Purity: Purified from mouse ascites fluids or tissue culture supernatant by affinity chromatography (protein A/G)

Pathway: N/A