GBE1 monoclonal Antibody | MB63385

GBE1 monoclonal Antibody | MB63385 | Gentaur UK, US & Europe Distribution

Host: Mouse

Reactivity: Human, Mouse, Rat

Application: IHC, IP, WB

Application Range: WB 1:2000, IHC 1:50, IP 2ug/500ul

Background: The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease) . [provided by RefSeq]

Storage & Stability: PBS (pH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Specificity: glucan (1,4-alpha-), branching enzyme 1

Molecular Weight: 80.3 kDa (Predicted)

Note: For research use only, not for use in diagnostic procedure.

Alternative Names: APBD; GBE; GSD4

Immunogen: Full length human recombinant protein of human GBE1 (NP_000149) produced in HEK293T cell.

Conjugate: Unconjugated

Modification: Unmodification

Purification & Purity: Purified from mouse ascites fluids or tissue culture supernatant by affinity chromatography (protein A/G)

Pathway: N/A