HADHSC Antibody | XW-8005

HADHSC Antibody | XW-8005 | Gentaur UK, US & Europe Distribution

Host: Chicken

Reactivity: Human, Mouse, Rat

Homology: N/A

Immunogen: 57-314

Research Area: Other

Tested Application: WB

Application: Short chain 3-hydroxyacyl-CoA dehydrogenase, mitochondrial antibody can be used for the detection of Short chain 3-hydroxyacyl-CoA dehydrogenase, mitochondrial by Western Blot.

Specificiy: N/A

Positive Control 1: N/A

Positive Control 2: N/A

Positive Control 3: N/A

Positive Control 4: N/A

Positive Control 5: N/A

Positive Control 6: N/A

Molecular Weight: 34.3 kDa (calculated)

Validation: N/A

Isoform: N/A

Purification: Immunoaffinity Purified

Clonality: Polyclonal

Clone: N/A

Isotype: N/A

Conjugate: Unconjugated

Physical State: Liquid

Buffer: Phosphate-Buffered Saline. No preservatives added.

Concentration: 1 mg/mL

Storage Condition: HADHSC antibody can be stored at 4˚C for short term (weeks) . Long term storage should be at -20˚C. As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.

Alternate Name: HAD, HADHSC, SCHAD, Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial, Medium and short-chain L-3-hydroxyacyl-coenzyme A dehydrogenase, HCDH, Short chain 3hydroxyacylCoA dehydrogenase, Medium and short chain L-3-hydroxyacyl-coenzyme A dehydrogenase

User Note: Optimal dilutions for each application to be determined by the researcher.

BACKGROUND: FUNCTION: Plays an essential role in the mitochondrial β-oxidation of short chain fatty acids. Exerts it highest activity toward 3-hydroxybutyryl-CoA.

DISEASE: Defects in HADHSC are the cause of 3-α-hydroxyacyl-CoA dehydrogenase deficiency (HAD deficiency) [MIM:609609]. HAD deficiency is a metabolic disorder with various clinical presentations including hypoglycemia, hepatoencephalopathy, myopathy or cardiomyopathy, and in some cases sudden death.