Carglumic acid | B2447

Carglumic acid is an activator of carbamoyl phosphate synthetase 1 (CPS1), the first enzyme in the urea cycle that is responsible for removal and detoxification of ammonia, making this drug a valuable agent for therapy of hyperammonemia caused by rare forms of urea cycle defects.

Carglumic acid is an activator of carbamoyl phosphate synthetase 1 (CPS1), the first enzyme in the urea cycle that is responsible for removal and detoxification of ammonia, making this drug a valuable agent for therapy of hyperammonemia caused by rare forms of urea cycle defects.

B2447 | Carglumic acid DataSheet

Alternate Name/Synonyms: N-(aminocarbonyl)-L-glutamic acid, N-Carbamyl-L-Glutamic Acid

Appearance: White to off-white solid

Formulation:

CAS Number: 1188-38-1

Structure Available?:

Peptide sequence: N/A

Salt Form: No

Molecular Formula: C₆H₁₀N₂O₅

Molecular Weight: 190.15

Cell-Permeable?: True

Purity: ≥98%

Solubilities: ~30 mg/ml DMSO

Handling: Do not take internally. Wear gloves and mask when handling the product! Avoid contact by all modes of exposure.

Country of Origin: USA

Tag Line: An activator of carbamoyl phosphate synthetase 1 (CPS1)

MDL Number:

PubChem CID: 121396

SMILES: C(CC(=O)O)C(C(=O)O)NC(=O)N

InChi: InChI=1S/C6H10N2O5/c7-6(13)8-3(5(11)12)1-2-4(9)10/h3H,1-2H2,(H,9,10)(H,11,12)(H3,7,8,13)/t3-/m0/s1

InChi Key: LCQLHJZYVOQKHU-VKHMYHEASA-N