FKRP Antibody | 13-491

FKRP Antibody | 13-491 | Gentaur UK, US & Europe Distribution

Host: Rabbit

Reactivity: Human, Mouse, Rat

Homology: N/A

Immunogen: Recombinant fusion protein containing a sequence corresponding to amino acids 30-220 of human FKRP (NP_077277.1) .

Research Area: Signal Transduction

Tested Application: WB, IHC

Application: WB: 1:1000 - 1:3000
IHC: 1:50 - 1:200

Specificiy: N/A

Positive Control 1: U-87MG

Positive Control 2: LO2

Positive Control 3: A-549

Positive Control 4: HT-29

Positive Control 5: 293T

Positive Control 6: N/A

Molecular Weight: Observed: 45kDa

Validation: N/A

Isoform: N/A

Purification: Affinity purification

Clonality: Polyclonal

Clone: N/A

Isotype: IgG

Conjugate: Unconjugated

Physical State: Liquid

Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

Concentration: N/A

Storage Condition: Store at -20˚C. Avoid freeze / thaw cycles.

Alternate Name: Fukutin-related protein, 2---, FKRP

User Note: Optimal dilutions for each application to be determined by the researcher.

BACKGROUND: This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined.