GAA Antibody (N-term) [AMM04653G]

GAA Antibody (N-term) [AMM04653G] | Gentaur UK, US & Europe Distribution

Product Category: Polyclonal Antibodies

Host: Rabbit

Species Reactivity: H

Specificity: This GAA antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 174-203 amino acids from the N-terminal region of human GAA.

Cellular Localisation: Lysosome. Lysosome membrane

Molecular Weight: 105324

Clone: Polyclonal

Gene Name: GAA

Gene ID: 2548

Function: Essential for the degradation of glycogen in lysosomes (PubMed:1856189, PubMed:7717400, PubMed:14695532, PubMed:18429042) . Has highest activity on alpha-1, 4-linked glycosidic linkages, but can also hydrolyze alpha-1, 6-linked glucans (PubMed:29061980) .

Summary: N/A

Form: Purified polyclonal antibody supplied in PBS with 0.09% (W/V) sodium azide. This antibody is purified through a protein A column, followed by peptide affinity purification.

Storage: Maintain refrigerated at 2-8°C for up to 2 weeks. For long term storage store at -20°C in small aliquots to prevent freeze-thaw cycles.

Application: IHC-P-Leica, IHC, WB

Dilution: IHC-P-Leica--1:500 WB--1:1000

Synonyms: Lysosomal alpha-glucosidase, Acid maltase, Aglucosidase alfa, 76 kDa lysosomal alpha-glucosidase, 70 kDa lysosomal alpha-glucosidase, GAA