BW
Sarcoglycanγ polyclonal Antibody | BS91205
- SKU:
- BW-BS91205
- Availability:
- Usually ships in 5 working days
Description
Sarcoglycanγ polyclonal Antibody | BS91205 | Gentaur UK, US & Europe Distribution
Host: Rabbit
Reactivity: Human, Mouse
Application: WB IP IHC
Application Range: WB:1:500-1:2,000 IP:1:50-1:100 IHC:1:50-1:200
Background: The sarcoglycan transmembrane proteins are members of the dystrophin complex. Sarcoglycans cluster together to form a complex, which is localized in the cell membrane of skeletal, cardiac and smooth muscle fibers. Four sarcoglycan subunit proteins, designated α-, β-, γ- and δ-sarcoglycan, form a complex on the skeletal muscle cell surface membrane. A genetic defect in any one of these proteins causes the loss or marked decrease of the whole sarcoglycan complex, which is observed in the autosomal recessive muscular dystrophy, sarcoglycanopathy. In smooth muscle, β- and δ-sarcoglycans are associated with ε-sarcoglycan, a glycoprotein homologous to α-sarcoglycan. Additionally, a complete deficiency in δ-sarcoglycan is the cause of the Syrian hamster BIO.14 cardiomyopathy.
Storage & Stability: Store at +4°C after thawing. Aliquot store at -20°C or -80°C. Avoid repeated freeze / thaw cycles.
Specificity: Sarcoglycanγ polyclonal Antibody detects endogenous levels of Sarcoglycanγ protein.
Molecular Weight: 32 kDa
Note: For research use only, not for use in diagnostic procedure.
Alternative Names: Gamma-SG, 35DAG, SGCG, 35 kDa dystrophin associated glycoprotein, 35 kDa dystrophin-associated glycoprotein, 35DAG, 35kD dystrophin associated glycoprotein, 35kDa dystrophin-associated glycoprotein, A4, DAGA4, DMDA, DMDA1, Gamma SG, Gamma-sarcoglycan, Gamma-SG, LGMD2C, MAM, MGC130048, Sarcoglycan gamma, SCARMD2, SCG3, SGCG, SGCG, TYPE,
Immunogen: recombinant protein
Conjugate: Unconjugated
Modification: Unmodification
Purification & Purity: ProA affinity purified
Pathway: